Purpose: To describe a patient with acinic cell carcinoma of the lacrimal g
land presenting with atypical manifestations including erosion of the orbit
al roof and intracranial extension. We compare his clinical manifestations
with two previously reported cases.
Methods: Case report.
Results. A 51-year-old man presented with a firm, tender, palpable mass in
the superior temporal portion of his right orbit. CT scan demonstrated a la
rge homogeneously enhancing mass displacing the globe inferiorly and erodin
g the roof of the orbit. MRI of the orbit showed intracranial extension of
tumor. Biopsy revealed an acinic cell carcinoma of the lacrimal gland.
Conclusions: Acinic cell carcinoma is a rare neoplasm occurring primarily i
n the major and minor salivary glands.