Background. Malignant triton tumor is usually an aggressive sarcoma consist
ing of a malignant schwannoma with rhabdomyoblastic differentiation. Howeve
r, malignant triton tumor of the nasal cavity is very rare.
Methods. A case report of a 38-year-old woman with polypoid mass, which ble
d easily in the right nasal cavity, and nasal obstruction is presented with
a review of the literature pertaining to this unusual case.
Results. The malignant triton tumor was treated with wide surgical excision
followed by radiation therapy. Histopathological diagnosis of the malignan
t triton tumor was made on the surgical specimen. The patient's postoperati
ve course was unremarkable, and follow-up at 5 years reveals no evidence of
Conclusions. A malignant triton tumor in the nasal cavity is a rare disease
. Head and neck surgeons should recognize the possibility of malignant trit
on tumor occurring in the nasal cavity. (C) 2001 John Wiley & Sons, Inc.