Acrocyanosis: changing concepts and nosological limitations

Citation
B. Planchon et al., Acrocyanosis: changing concepts and nosological limitations, J MAL VASC, 26(1), 2001, pp. 5-15
Citations number
53
Language
FRANCESE
art.tipo
Article
Categorie Soggetti
Cardiovascular & Respiratory Systems
Journal title
JOURNAL DES MALADIES VASCULAIRES
ISSN journal
0398-0499 → ACNP
Volume
26
Issue
1
Year of publication
2001
Pages
5 - 15
Database
ISI
SICI code
0398-0499(200102)26:1<5:ACCANL>2.0.ZU;2-2
Abstract
Acrocyanosis is undoubtedly the most commonplace acrosyndrome, both in term s of pathogenesis and prognosis. Patients experience functional impairment and an esthetic prejudice that must not be neglected. Adopting the nosologi cal classifications described for Raynaud's syndrome, primary acrocyanosis must be distinguished from exceptional secondary phenomena that have a radi cally different clinical course. Primary acrycyanosis is generally observed in a youngs women who appears thin or has recently lost weight. No paroxys mal episode (syncope, cyanosis, suspicious event involving the fingers) is found. The physical examination is negative and no complementary exploratio ns are needed. Current pathophysiological hypotheses remain insufficient bu t suggest that vasopasticity rather than hemorheology is involved. The hypo thesis that a thermoregulation disorder could be associated with weight los s deserves further study. Symptomatic care relies on dietary and hygiene co unseling, emphasizing the importance of warm clothing. The psychological el ement must also be considered even in the most common forms.