Congenital hepatic artery-to-portal vein fistula, a rare type of arterioven
ous malformation that may be intrahepatic or extrahepatic, is an uncommon c
ause of severe infantile portal hypertension. Many researchers believe that
acquired intrahepatic arterioportal fistulas are best treated by embolizat
ion and that extrahepatic arterioportal fistulas require surgical intervent
ion. The experience with congenital intrahepatic arterioportal fistulas is
very limited and has required both embolization and surgical intervention.
We report a case of solitary congenital arterioportal fistula successfully
treated with coil embolization.