Rupture of the abdominal aorta in patients with Ehlers-Danlos syndrome

Citation
Cd. Karkos et al., Rupture of the abdominal aorta in patients with Ehlers-Danlos syndrome, ANN VASC S, 14(3), 2000, pp. 274-277
Citations number
20
Language
INGLESE
art.tipo
Article
Categorie Soggetti
Surgery
Journal title
ANNALS OF VASCULAR SURGERY
ISSN journal
0890-5096 → ACNP
Volume
14
Issue
3
Year of publication
2000
Pages
274 - 277
Database
ISI
SICI code
0890-5096(200005)14:3<274:ROTAAI>2.0.ZU;2-4
Abstract
Ehlers-Danlos syndrome (EDS) is a heterogenous inherited disorder of collag en synthesis. Type IV is frequently associated with major vascular catastro phes and challenges the vascular surgeon with its varied clinical presentat ion and the difficulty of vascular repair. Rupture of the abdominal aorta i s one of the most serious complications and is associated with nearly 100% mortality rate. We describe here three patients with type IV EDS. DOI:10.10 07/s100169910047.