Nonconvulsive status epilepticus in a child with congenital bilateral perisylvian syndrome

Citation
T. Tagawa et al., Nonconvulsive status epilepticus in a child with congenital bilateral perisylvian syndrome, PED NEUROL, 21(2), 1999, pp. 579-582
Citations number
13
Language
INGLESE
art.tipo
Article
Categorie Soggetti
Pediatrics,"Medical Research General Topics
Journal title
PEDIATRIC NEUROLOGY
ISSN journal
0887-8994 → ACNP
Volume
21
Issue
2
Year of publication
1999
Pages
579 - 582
Database
ISI
SICI code
0887-8994(199908)21:2<579:NSEIAC>2.0.ZU;2-2
Abstract
A 9-year-old male with congenital bilateral perisylvian syndrome is describ ed. He had pseudobulbar palsy, mental retardation, and intractable epilepsy . Computed tomography and magnetic resonance images of the brain demonstrat ed bilateral perisylvian malformations and a diffuse pachygyric appearance. At 8 years of age, he had episodes of excessive drooling, fluctuating impa irment of consciousness, unsteady sitting, and frequent head drop that last ed several days, The electroencephalogram demonstrated continuous diffuse s low spike and waves. These findings suggested atypical absence status epile pticus. Intravenous administration of diazepam resulted in transient improv ement of clinical and electroencephalographic findings. Status epilepticus recurred within several minutes after diazepam administration. Although no patient has been reported to have a history of status epilepticus among tho se affected by this syndrome, it seems that atypical absence status can occ ur more frequently than expected, as seen in Lennox-Gastaut syndrome. After recognition and confirmation of nonconvulsive status epilepticus, immediat e treatment must be attempted. (C) 1999 by Elsevier Science Inc. All rights reserved.