Syntelencephaly associated with connected transhemispheric cleft of focal cortical dysplasia

Citation
S. Fujimoto et al., Syntelencephaly associated with connected transhemispheric cleft of focal cortical dysplasia, PED NEUROL, 20(5), 1999, pp. 387-389
Citations number
11
Language
INGLESE
art.tipo
Article
Categorie Soggetti
Pediatrics,"Medical Research General Topics
Journal title
PEDIATRIC NEUROLOGY
ISSN journal
0887-8994 → ACNP
Volume
20
Issue
5
Year of publication
1999
Pages
387 - 389
Database
ISI
SICI code
0887-8994(199905)20:5<387:SAWCTC>2.0.ZU;2-3
Abstract
The authors report a female with syntelencephaly associated with a connecte d transhemispheric cleft of focal cortical dysplasia. Syntelencephaly is a rare anomaly characterized by fusion of the hemispheres in the posterior fr ontal and parietal regions and is considered a new variant of holoprosencep haly. Cranial magnetic resonance imaging of the patient revealed syntelence phaly associated with bilateral fused clefts of focal cortical dysplasia wi thout the pial-ependymal seam, which was regarded as an incomplete type of schizencephaly. The underlying mechanism is discussed. (C) 1999 by Elsevier Science Inc. All rights reserved.