An 11-month-old boy presented with recurrent wheezing and atelectasis in th
e right upper lobe of the lung. Bronchoscopy and bronchography confirmed an
ectopic bronchus arising from the right main bronchus. The diagnosis of VA
TER association was made on the basis of multiple vertebral and rib anomali
es, imperforate anus with a perineal fistula, unilateral hydronephrosis, at
rial septal defect, and a preauricular tag, he did not have tracheo-esophag
eal fistula. We emphasize the importance of recognizing tracheobronchial an
omalies in VATER association. (C) 1999 Wiley-Liss, Inc.