We report herein a case of familial primary hyperparathyroidism diagnosed i
n a 23-year-old woman who presented with hypercalcemia and urolithiasis. Th
e parathyroid gland was removed, and pathological examination revealed chie
f cell adenoma. The proband's younger sister had undergone surgery for para
thyroid adenoma at the age of 19, and her aunt had a history of urolithiasi
s with a high level of serum parathyroid hormone. We have not Set found evi
dence of any other endocrine disorders suggesting multiple endocrine neopla
sia (MEN) type 1 in this pedigree.