FAMILIAL VESTIBULOPATHY - A NEW DOMINANTLY INHERITED SYNDROME

Citation
Rw. Baloh et al., FAMILIAL VESTIBULOPATHY - A NEW DOMINANTLY INHERITED SYNDROME, Neurology, 44(1), 1994, pp. 20-25
Citations number
23
Language
INGLESE
art.tipo
Article
Categorie Soggetti
Clinical Neurology
Journal title
Neurology → ACNP
ISSN journal
0028-3878
Volume
44
Issue
1
Year of publication
1994
Pages
20 - 25
Database
ISI
SICI code
0028-3878(1994)44:1<20:FV-AND>2.0.ZU;2-K
Abstract
Three patients who presented with episodic vertigo followed by gait im balance and oscillopsia had profound bilateral vestibular lass despite normal hearing. All had a parent with similar findings. The patients, their affected parent, and multiple other family members had a histor y of migraine headaches, although several of the latter had normal ves tibular function. Acetazolamide stopped or markedly decreased the freq uency of vertigo attacks in the three patients treated but had little effect on the chronic vestibular loss. This is the first report of a d ominantly inherited bilateral vestibulopathy associated with normal he aring.