An 18-month-old girl with lesions in the cortex of the bilateral tibia
e and ulnae and right fibula is reported. The lesion in the right tibi
a disappeared after curettage and xenogeneic bone grafting, and the ot
her lesions disappeared spontaneously by the age of 12 years. All lesi
ons involved the bone cortex. The right tibial lesion exhibited the hi
stopathological features of ''zonal architecture'' and a osteoblast ri
m formation around the trabeculae. We consider that osteofibrous dyspl
asia can involve systemically any long bone.